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- Searching for "551" in the Protein Name field will retrieve all mutations that alter the protein at position 551.
- Searching for "del" in Mutation Names will retrieve all deletion mutations (but it may take awhile).
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cDNA Name
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Protein Name
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Legacy Name
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Region
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Description
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Consequence
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c.(?_744)_(2988_?)dup
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exon 7 - exon 18
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Duplication of exons 6B to 16
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c.-593A>G
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- 461A- >G
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promoter
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A to G at - 461
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promoter mutation
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c.-410g>C
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promoter
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c.1A>C
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p.Met1Leu
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M1L
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exon 1
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A to C at 133
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Met to Leu at 1
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c.53+4A>T
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185+ 4A- >T
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intron 1
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A to T at 185+ 4
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mRNA splicing defect? (CBAVD)
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c.54-4235_164+377dup4723
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intron 1
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c.54-1G>A
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intron 1
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c.76A>G
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p.Lys26Glu
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exon 3
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c.79G>C
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p.Gly27Arg
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G27R(211G to C)
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exon 2
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G to C at 211
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Gly to Arg at 27
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c.79G>A
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p.Gly27Arg
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G27R
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exon 2
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G to A at 211
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Gly to Arg at 27
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c.224G>T
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p.Arg75Leu
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R75L
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exon 3
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G to T at 356
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Arg to Leu at 75
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c.325T>C
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p.Tyr109His
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exon 4
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c.338A>T
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p.Asn113Ile
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N113I
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exon 4
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A to T at 470
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Asn to Ile
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c.387delT
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p.Leu130SerfsX?
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519delT
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exon 4
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T deleted
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frameshift
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c.442A>T
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p.Ile148Phe
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exon 4
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c.446G>T
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p.Gly149Val
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G149V
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exon 4
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G to T at 578
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Gly to Val at 149
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c.451C>A
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p.Gln151Lys
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Q151K
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exon 4
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C to A at 583 (CAG- >AAG)
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Gln to Lys at 151
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c.476T>C
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p.Leu159Ser
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L159S
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exon 4
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T to C at 608
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Leu to Ser at 159
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c.490-2A>G
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622- 2A- >G
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intron 4
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A to G at 622- 2
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mRNA splicing defect
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c.500T>G
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p.Leu167Arg
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exon 5
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c.533G>A
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p.Gly178Glu
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G178E
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exon 5
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G to A at 665
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Gly to Glu at 178
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c.606G>A
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p.Trp202X
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W202X
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exon 6
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G to A at 738
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Try to Stop at 202
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c.744-2a>G
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intron 6
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c.829T>A
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p.Trp277Arg
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W277R
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exon 7
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T to A at 961
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Trp to Arg at 277
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c.869+5g>A
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intron 7
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c.890G>A
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p.Arg297Gln
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R297Q
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exon 8
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G to A at 1022
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Arg to Gln at 297
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c.938C>A
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p.Ser313X
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S313X
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exon 8
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C to A at 1070
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Ser to Stop
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c.1086T>A
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p.Tyr362X
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exon 8
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c.1116+1G>A
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1248+ 1G- >A
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intron 8
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G to A at 1248+ 1
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mRNA splicing defect
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c.1117-1g>A
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intron 8
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c.1227delT
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p.Phe409LeufsX33
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exon 10
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c.1324A>T
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p.Lys442X
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exon 10
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c.1331T>C
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p.Ile444Thr
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I444T
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exon 10
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T to C at 1463
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lle to Thr at 444
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c.1720C>T
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p.Pro574Ser
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P574S
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exon 13
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C to T at 1852
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Pro to Ser at 574
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c.1763A>T
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p.Glu588Val
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E588V
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exon 13
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A to T at 1895
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Glu to Val at 588
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c.1784T>C
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p.Met595Thr
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M595T
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exon 14
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T to C at 1916
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Met to Thr at 595
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c.2044delA
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p.Thr682GlnfsX40
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exon 14
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c.2087A>G
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p.Lys696Arg
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exon 14
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c.2233G>T
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p.Gly745X
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G745X(Gly745X)
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exon 14
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G to T at 2365
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Non-sense mutation
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c.2277delC
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p.Thr760ArgfsX11
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2409delC
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exon 14
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Deletion of C at 2409
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Frameshift
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c.2295G>T
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p.Arg765Ser
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exon 14
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c.2380delG
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p.Val794CysfsX9
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2512delG
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exon 14
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Deletion of G at 2512
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Frameshift
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c.2620-15C>G
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2752- 15C/G
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intron 15
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C or G at 2752- 15
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sequence variation
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c.2803_2813delCTACCACTGGT
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p.Leu935AlafsX36
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exon 17
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c.2918T>A
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p.Leu973His
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L973H
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exon 18
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T to A at 3050
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Leu to His at 973
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c.2988+33g>T
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3120+ 33G>T
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intron 18
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c.2989-3C>G
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3121- 3C- >G
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intron 18
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C to G at 3121- 3
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mRNA splicing
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c.3009_3017delAGCTATAGC
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p.Ala1004_Ala1006del
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3141del9
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exon 19
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del AGCTATAGC from 3141
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Frameshift
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c.3139+42A>T
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3271+ 42A/T
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intron 19
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A or T at 3271+ 42
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sequence variation
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c.3151A>G
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p.Ile1051Val
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I1051V
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exon 20
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A to G at 3283
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Ile to Val at 1051
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c.3196C>T
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p.Arg1066Cys
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R1066C
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exon 20
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C to T at 3328
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Arg to Cys at 1066
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c.3199G>C
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p.Ala1067Pro
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A1067P
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exon 20
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G to C at 3331
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Ala en Pro at 1067
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c.3304A>T
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p.Arg1102X
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R1102X
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exon 20
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A to T at 3436
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Arg to Stop at 1102
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c.3443A>G
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p.Asn1148Ser
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N1148S
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exon 21
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A to G at 3575
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Asn to Ser at 1148
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c.3469-331_3469-295del37;3469-189_3717+3822del4260pb
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intron 21 - exon 22
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c.3717G>C
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p.Arg1239Ser
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R1239S
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exon 22
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G to C at 3849
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Arginine to Serine at 1239
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c.3835_3836delTT
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p.Leu1279AlafsX22
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exon 23
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c.3837G>A
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p.Leu1279Leu
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exon 23
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c.3847A>G
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p.Arg1283Gly
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exon 23
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c.3964-78_4242+577del
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CFTRdele22, 23
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exon 25 - exon 26
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This deletion extends from nucleotide - 78 of intron 21 (the end of intron 21 being defined as - 1) to nucleotide + 577 of intron 23 (the beginning of intron 23 being defined as + 1) with a loss of 1532 nucelotides
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The loss of exons 22 and 23 was in-frame and was predicted to result in a CFTR protein lacking amino acids 1322 to 1414, this constitutes the carboxy terminal end of the newly defined nucleotide-binding domain (NBD) 2 of the protein
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c.3963+2t>A
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intron 24
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c.4035_4038dupCCTA
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p.Ser1347ProfsX13
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exon 25
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c.4196_4197delTC
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p.Cys1400X
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4326delTC
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exon 26
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Deletion of TC from 4326 to 4327
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FrameShift
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c.4242+1G>A
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4374+ 1G- >A
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intron 26
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G to A at 4374+ 1
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mRNA splicing defect
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c.4243-7delT
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4375- 7delT
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intron 26
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c.4252G>T
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p.Glu1418X
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E1418X
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exon 27
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G to T at 4384 (GAG- >TAG)
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Glu to Stop at 1418
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c.2989-977_3367+248del
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3121- 977_3499+ 248del2515
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exon 19 - exon 20
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3121- 977_3499+ 248del2515bp
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Large deletion removing exons 17a and 17b. Frameshift
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c.(?_1211)_(2988_?)dup
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CFTRdup10_18
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exon 11 - exon 21
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Duplication of exons 10 to 18
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The position and orientation of the duplicated region have not been determined. However, given the classical CF phenotype, it is hypothesized that it is located inside the CFTR gene.
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c.(?_2620)_(3367_?)del
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CFTRdele14b- 17b
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exon 16 - exon 20
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9890 bp deletion
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Removes 5 coding exons
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c.(?_274)_(743_?)delins6
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CFTRdele4- 6aIns6bp
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exon 4 - exon 6
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Deletion of 18, 654 bp encompassing exons 4, 5, and 6a, together with an insertion of 6 bp
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This large deletion disrupted the reading frame of the protein
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c.2620-674_3367+198del
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2752- 674_3499+ 198del9855
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exon 16 - exon 20
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2752- 674_3499+ 198del9855bp
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Large deletion removing exons 14b to 17b. Frameshift
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c.(?_274)_(489_?)delins41
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CFTRdele4Ins41bp
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exon 4
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Gross deletion of 8, 165 bp spanning exon 4, together with an insertion of 41 bp
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This deletion was in-frame and was predicted to lead to the synthesis of a protein lacking amino acids 92-163, a stretch that includes a part of TM1 and the the entire TM2
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c.4_53+69delins299
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CFTRdele1 or 136del119ins299
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exon 1 - intron 1
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136_185+ 69del119bpins299bp
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Deletion of exon 1 from nucleotide 136 (codons 2-18) to intron 1 nucleotide +69 and insertion of an inverted and complementary sequence of intron 1 (nucleotide 185+4191 to +4488) and addition of a G at the junction. A small peptide of 17 residues if translation starts at the same ATG or another protein (possibly CFTR-like?) if another ATG is choosen.
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c.4_53+69delins299
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CFTRdele1Ins299bp
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exon 1
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This indel involved the deletion of 119 bp extending from coding position 4 (A of the ATG- translation initiation codon being defined as 1) to IVS1+ 69 that removed nearly the entire coding sequence of exon 1, and the insertion of 299 bp at the deletion junction
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c.4_53+69delins299
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CFTRdele1
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exon 1
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Deletion of exon 1 from nucleotide 136 (codons 2- 18) to intron 1 nucleotide + 69 and insertion of an inverted and complementary sequence of intron 1 (nucleotide 185+ 4191 to + 4488) and addition of a G at the junction.
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A small peptide of 17 residues if translation starts at the same ATG or another protein (possibly CFTR-like?) if another ATG is choosen.
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c.(?_-132)_(273_?)dup
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CFTRdup1- 3
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exon 1 - exon 3
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Duplication of exons 1 to 3
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Large rearrangement. The break points and orientation are being assessed
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c.33281_3367+268del355insTGTTAA
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3413del355_insTGTTAA
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exon 20
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Partial deletion of exon 17b. It removes 355 bp, i.e. from nt 3413 (in codon 1094) to 3499+ 268 in intron 17b; the sequence "TGTTAA" is inserted at the breakpoints.
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A stop codon appears very early in the new sequence but the consequences at the RNA level remain to be studied.
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c.-12_10del23
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120del23
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promoter - exon 1
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Deletion of 23 bp from nucleotide + 120 of exon 1 promoter, to nucleotide 142 (the first nucleotide of codon 4)
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This mutation abolishes the initiation codon at position 133. The next possible initiation codon is located at intron 1 position 185+63.
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